Anti-Fibrillin 1 Anticorpo [FBN1/6933] (A314965)

Anti-Fibrillin 1 Antibody [FBN1/6933]

Mouse monoclonal [FBN1/6933] antibody to Fibrillin 1.

Fibrillin-1 is an extracellular matrix glycoprotein that serves as a structural component of calcium-binding microfibrils. These microfibrils provide force-bearing structural support in elastic and non-elastic connective tissue throughout the body.Mutations in this gene are associated with Marfan syndrome.

ELISA, IHC-P

HepG2 cells. Human kidney or placenta.

IHC: 1-2 µg/ml

Human

Recombinant human Fibrillin 1 fragment around Amino Acids 330-476. The exact sequence is proprietary.

Mouse

Monoclonal

FBN1/6933

IgG1

Unconjugated

Protein A/G chromatography.

200 µg/ml

350 kDa

Liquid

Supplied in 10mM Phosphate Buffered Saline with 0.05% BSA and 0.05% Sodium Azide.

Shipped at 4°C. Upon delivery aliquot and store at -20°C. Avoid freeze / thaw cycles.

350 kDa glycoprotein component extracellular microfibril, ACMICD, FBN, FBN 1, FBN1, FBN1_HUMAN, Fibrillin 15, Fibrillin-1, Fibrillin1, Fibrillin15, GPHYSD2, Marfan syndrome, MASS, MFS 1, MFS1, OCTD, SGS, SSKS, Weill Marchesani syndrome, WMS, WMS2